中文名稱:ACOX2 抗原(重組蛋白)
英文名稱: ACOX2 Antigen (Recombinant Protein)
別 名: Acyl-CoA oxidase 2, branched chain; BCOX; BRCOX; THCCox; BRCACOX
儲 存: 冷凍(-20℃)
相關類別: 抗原
概 述:
Fusion protein corresponding to C terminal 250 amino acids of human ACOX2 |
Full name: |
Acyl-CoA oxidase 2, branched chain |
Synonyms: |
BCOX; BRCOX; THCCox; BRCACOX |
Swissprot: |
Q99424 |
Gene Accession: |
BC047700 |
Purity: |
>85%, as determined by Coomassie blue stained SDS-PAGE |
Expression system: |
Escherichia coli |
Tags: |
His tag C-Terminus, GST tag N-Terminus |
Background: |
The product of this gene belongs to the acyl-CoA oxidase family. It encodes the branched-chain acyl-CoA oxidase which is involved in the degradation of long branched fatty acids and bile acid intermediates in peroxisomes. Deficiency of this enzyme results in the accumulation of branched fatty acids and bile acid intermediates, and may lead to Zellweger syndrome, severe mental retardation, and death in children. |